Myxosarcoma complicating a cystic hamartoma of the lung.
نویسندگان
چکیده
Primary myxomas and myxosarcomas of the lung are very rare. Stout studied in 1948 the records of Columbia University and the cases reported in the world literature and was able to collect 140 cases but there were no myxomas arising from the lung or pleura. Miller and Jackson (1954) reported a case of myxosarcoma of the lung and Barkley and Cardozo (1957) published another case of myxomatous tumour of the lingula extending to the pleura. We have observed, and report herewith, a case of myxosarcoma arising from a congenital cyst of the lung and the histological findings confirm that this is a cystic hamartoma. Cystic hamartomas are rare dysplastic tumours of the lung and they appear usually in premature infants. These tumours are also reported as adenomatous hyperplasiae (Ch'in and Tang, 1949). In newborn babies and infants they can be very large, occupying a whole lobe or lung, as distinct from the hamartomas of the adult which are usually smaller and circumscribed (Hochberg and Schacter, 1957). Cystic hamartomas are characterized by the overgrowth of bronchioles which causes lobar enlargement, while the development of the alveoli is suppressed except at the periphery (Campbell, 1957). These neoplasms grow into large cysts because of the development of a valvular mechanism, and it is then difficult to distinguish them radiologically from obstructive emphysematous cysts. Malignant degeneration developing in congenital cysts of the lung, such as bronchogenic cysts, has been reported. But in all cases histological examination proved the presence of bronchial carcinoma (Womack and Graham, 1941; Moersch and Clagett, 1947; Korol, 1953; Murphy and Piver, 1951; Bass and Singer, 1951; Larkin and Phillips, 1955; West and Van Schoonhoven, 1957; Tala and Laustela, 1958). Myxomatous degeneration of a cyst of the lung has not been recorded in the literature.
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عنوان ژورنال:
- Thorax
دوره 18 شماره
صفحات -
تاریخ انتشار 1963